Dementia with Lewy bodies is a common form of dementia that remains underdiagnosed and poorly understood by most health-care professionals. The general practitioner will often mbe the first doctor that patients or their concerned relatives see. A few fairly simple signs and symptoms should raise suspicions of the diagnosis. The general practitioner can offer invaluable support and information to the patient and their family, including advanced care planning. Drug treatment for this disease is limited, although useful in selected cases. A large amount of research is being conducted into this form of dementia that will hopefully lead to improved treatments.